Hydatid disease, a zoonotic infection caused by a tapeworm of the genus Echinococcus, has been encountered in various organs in humans. In spite of all the advances in imaging techniques and therapeutic methods, hydatidosis of the central nervous system is still a life-threatening condition in infested areas of the world. Geographical regions affected include the Middle East, Mediterranean countries, South America, Central and Eastern Europe, South Africa, India, and Australia.

Historical Aspects of Hydatidosis of Central Nervous system.- Hydatidosis of Central Nervous System in Mediterranean Countries and Middle East.- Hydatidosis of Central Nervous System in South America.- Hydatidosis of Central Nervous System in Central and Eastern Europe.- Clinical Manifestations of Hydatidosis of Central Nervous System.- Hydatidosis of the Skull.- Hydatidosis of the Brain.- Intraventricular Hydatidosis.- Hydatidosis of the Spinal Cord.- Hydatidosis of the Spine.- Laboratory Findings of Patients with Hydatidosis of Central Nervous System.- Imaging of Cerebral Hydatidosis Disease.- Imaging of Spinal Hydatid Disease.- In vivo Proton Magnetic Resonance Spectroscopy in Hydatidosis of the Central Nervous System.- Surgical Treatment of Spinal Hydatidosis.- Surgical Treatment of Cerebral Hydatidosis.- Chemotherapy for Hydatidosis of the Central Nervous System.- Complications of Cerebral Hydatidosis.- Complications of Spinal Hydatidosis.- Outcome and Follow-up of Patients with Cerebral Hydatidosis.- Outcome and Follow-up of Patients with Spinal Hydatidosis.- Unusual Presentations of Hydatidosis of the Central Nervous System.- Cerebrovascular Occlusive Disease: Hydatidosis.- Hydatidosis of the Orbit.- Alveolar Hydatidosis of the Central Nervous System.- Prevention and Control of Hydatidosis.